Genetic analysis of four cases of methylmalonic aciduria and homocystinuria, cblC type#.

نویسندگان

  • Jun Wang
  • Erzhen Li
  • Liwen Wang
  • Zhilong Wang
  • Shenghai Yang
  • Qiao Zhou
  • Qian Chen
چکیده

Methylmalonic aciduria and homocystinuria, cblC type, is the most common disorder of intracellular vitamin B12 (cobalamin, cbl) metabolism, which results in impaired biosynthesis of methylcobalamin and adenosylcobalamin. The gene MMACHC responsible for the cblC type had been identified, which enables molecular diagnostics. Here, we report four cblC type cases, which were identified by the typical manifestations, and a new approach of next-generation sequencing platform in pediatrics for genetic diseases, further confirmed by Sanger sequencing of the whole MMACHC gene. The article will replenish the mutational information of related genes to the cblC type, which makes for detecting of cblC disease through the newborn screening.

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CblC Type Methylmalonic Aciduria with a Novel Homozygous Mutation: A Case Report

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عنوان ژورنال:
  • International journal of clinical and experimental pathology

دوره 8 8  شماره 

صفحات  -

تاریخ انتشار 2015